Citation Information :
Bector A, Kaur A, Acharya S, Rajpal S, Awasthi S. Prosthetic Rehabilitation of a 3 Year Old Child with Ectodermal Dysplasia — A Case Report. 2015; 3 (3):174-178.
Ectodermal dysplasia are rare hereditary disorders characterized by abnormal development of certain tissues and structures of ectodermal origin. Children affected need multidisciplinary approach and a removable prosthesis is recommended in initial years of life to prevent bone resorption, improve esthetics, mastication and speech apart from boosting self image. Implants are recommended only once the growth is complete. This case reports hypohidrotic ectodermal dysplasia with partial anodontia in a 3 year old child, rehabilitated with partial denture in maxillary and complete denture in mandibular arch.
Tarjan I, Gabris K and Rozsa N. Prosthetic treatment of patients with ectodermal dysplasia: A clinical report. J. Prosthet Dent 2005;93:419-424
Kramer F, Baethge C, Tschernitschek H. Implants in children with ectodermal dysplasia: A case report and literature Review. Clin Oral Impl Res 2007;18:140–6
Priolo M, Silengo M, Lerone M, Ravazzolo R. Ectodermal dysplasia: Not only ‘skin’ deep. Clin Genet 2000;58:415-30
Gupta S, Tyagi P. Prosthodontic management of anhidrotic ectodermal dysplasia. Indian J Dent Res 2011;22:348–51
Chang TT, Behsad R, Brodell RT, Gilliam AC. A male infant with anhidrotic ectodermal dysplasia/immunodeficiency accompanied by incontinentia pigmenti and a mutation in the NEM Opathway. J Am Acad Deramatol 2008;58:316-20
Bal E, Baala L, Cluzeau C, El Kerch F, Ouldim K, Hadj- Rabia S. Autosomal dominant anhidrotic ectodermal dysplasias at the EDARADD locus. Hum Mutat 2007;28:703-9
Available from: http://emedicine.medscape.com/article/1110595-overview
Vieira KA, Teixeiva MS, Guirado CG, Cariaro MB. Prosthodontic treatment of with complete anodontia: case report. Quintessence Int 2007;38:75-80
Acikgoz A, Kademoglu O, Elekdag-Turk S and Karagoz F. Hypohidrotic ectodermal dysplasia with true anodontia of the primary dentition. Quintessence Int 2007;38:853-85
Guckes A, Scurria M, McCarthy G, Brahim J. Prospective clinical trial of dental implants in persons with ectodermal dysplasia. J Prosthet Dent 2002;88:21–5
Celar AG, Durstberger G and Zauza K. Use of an individual traction prosthesis and distraction osteogenesis to reposition osseointegrated implants in a juvenile with ectodermal dysplasia: a clinical report. J Prosthet Dent 2002;87:145-148
Shaw WC. Problem of accuracy and reliabiltiy in cephalometric studies with implants in infants with cleft lip and palate. Br J Orthod 1977;4:93-100
Guckes AD, Brahim JS, McCarthy GR, Rudy SF and Cooper LF. Using endosseous dental implants for patients with ectodermal dysplasia. JADA 1939;122:59-62
Guckes AD, Roberts MW, McCarthy GR. Pattern of permanent teeth present in individuals with ectodermal dysplasia and severe hypodontia suggests treatment with dental implants. Pediatr Dent 1998; 20:278-80
Bergendal B, Koch G, Karol J, Wanndahl G. Consensus Conference on Ectodermal Dysplasia with special reference to Dental Treatment. Stockholm, Sweden: Forlagshuset Gothia AB; 1998
